Kanchi Kamakoti CHILDS Trust Hospital & The CHILDS Trust Medical Research Foundation, Nungambakkam, Chennai, India.
Saudi J Gastroenterol. 2011 May-Jun;17(3):212-4. doi: 10.4103/1319-3767.80387.
Biliary diversion offers a potential option for intractable pruritus in children with chronic cholestatic disorders. Progressive familial intrahepatic cholestasis (PFIC) is an inherited disorder of impaired bile acid transport and excretion, which presents with jaundice and pruritus in the first few months of life and progresses to cirrhosis by infancy or adolescence. We report a child with PFIC type 1 who underwent internal biliary diversion for intractable pruritus and was relieved of his symptoms.
胆道分流术为慢性胆汁淤积性疾病所致难治性瘙痒的患儿提供了一种潜在的选择。进行性家族性肝内胆汁淤积症(PFIC)是一种胆汁酸转运和排泄受损的遗传性疾病,患儿在生命最初几个月即出现黄疸和瘙痒,并在婴儿期或青春期进展为肝硬化。我们报告了一例 PFIC 1 型患儿,其因难治性瘙痒行内胆管分流术,症状得到缓解。