Limone P, Maccario M, Vigliani R, Isaia G, Massara F, Molinatti G M
Istituto di Medicina Interna, Università di Torino, Italy.
J Endocrinol Invest. 1990 Feb;13(2):171-5. doi: 10.1007/BF03349532.
Primary pigmented micronodular disease is a peculiar form of ACTH-independent Cushing's syndrome characterized by the familial occurrence, the frequent association with malformations and the pathological adrenocortical picture consisting in micronodules with cellular deposition of lipofuscinic pigment. We describe here a case occurring in a 14-year-old girl.
原发性色素沉着性微结节病是一种特殊形式的不依赖促肾上腺皮质激素的库欣综合征,其特征为家族性发病、常伴有畸形以及病理上肾上腺皮质表现为含脂褐素色素细胞沉积的微结节。我们在此描述一例发生于一名14岁女孩的病例。