非典型溶血尿毒综合征（HUS）在长期无尿后恢复：一例病例报告。
Atypical hemolytic-uremic syndrome (HUS) with recovery after a long-lasting anuria: a case report.
作者信息
Georgaki-Angelaki H, Stergiou N, Kapogiannis A, Orfanou I, Grapsa B, Roma E
出版信息
Hippokratia. 2011 Jan;15(1):90-2.
Abstract
We report a case of a seven-year-old girl who suffered from atypical Hemolytic Uremic Syndrome (aHUS) complicated by septicaemia, central nervous system involvement, and cholangiitis. She remained anuric requiring treatment with peritoneal dialysis (PD) for a five-month period. In addition to conventional therapeutic measures including fresh frozen plasma (FFP) and blood cells transfusions she also underwent to plasma exchange (PE) treatment. Following a stormy hospitalization period of 17 weeks, the patient finally regained renal function and three years later she remains well on antihypertensive treatment and free of dialysis.
摘要
我们报告了一例七岁女孩，她患有非典型溶血尿毒综合征（aHUS），并伴有败血症、中枢神经系统受累和胆管炎。她持续无尿，需要进行为期五个月的腹膜透析（PD）治疗。除了包括新鲜冰冻血浆（FFP）和输血在内的常规治疗措施外，她还接受了血浆置换（PE）治疗。经过17周的波折住院治疗后，患者最终恢复了肾功能，三年后，她在接受降压治疗且未进行透析的情况下状况良好。
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