Xia G
Zhonghua Yi Xue Za Zhi. 1990 Mar;70(3):128-9, 10.
Among 578 cases of Tetralogy of Fallot, 19 with absence left pulmonary artery were studied. When a patient has early and serious cyanosis and the stenosis of the outflow tract of right ventricle and/or the pulmonary artery is mild under echocardiographic examination, and at the same time, hemoglobin is markedly increased and SaO is rather low, the diagnosis of Tetralogy of Fallot with unilateral absence of pulmonary artery should be considered. The value of chest X-ray film is limited in this case. The diagnosis can be confirmed by selected angiography in the right ventricle which may reveal the anatomical deformity by the curved shadow or the drum-stick extremity in the left pulmonary artery.
在578例法洛四联症病例中，对19例左肺动脉缺如的病例进行了研究。当患者出现早期严重青紫，且超声心动图检查显示右心室流出道和/或肺动脉狭窄较轻，同时血红蛋白显著升高而血氧饱和度相当低时，应考虑单侧肺动脉缺如的法洛四联症诊断。在此病例中，胸部X线片的价值有限。通过选择性右心室造影可确诊，造影可能显示左肺动脉呈弧形阴影或杵状末端的解剖畸形。
