Zribi H, Brian E, Lenoir S, Validire P, Gossot D
Département Thoracique, Institut Mutualiste Montsouris, 42 Boulevard Jourdan, 75014 Paris, France.
Rev Mal Respir. 2011 May;28(5):672-6. doi: 10.1016/j.rmr.2010.12.005. Epub 2011 Apr 15.
Congenital bronchial atresia is a rare congenital obliteration of a segmental or lobar bronchus resulting in distension of the corresponding parenchyma. It is seldom diagnosed in the adult. It may lead to infectious complications and, in the long term, to damage to the adjacent lung parenchyma. A surgical resection is necessary and it can be achieved by thoracoscopy. We report a recent series of six patients.
先天性支气管闭锁是一种罕见的节段性或大叶性支气管先天性闭塞,导致相应实质组织扩张。在成人中很少被诊断出来。它可能导致感染性并发症,长期来看,还会损害相邻的肺实质。手术切除是必要的,可通过胸腔镜实现。我们报告了最近一组6例患者的情况。