Kumar Sunil Y, Shrikrishna U, Shetty Jayaprakash, Sitaram Aishwarya
Department of Pathology, KS Hegde Medical Academy, Deralakatte, Mangalore, India.
J Lab Physicians. 2011 Jan;3(1):56-8. doi: 10.4103/0974-2727.78571.
Epignathus is an extremely rare oropharyngeal teratoma that commonly arises from the palate, leading to a high mortality (80-100%) due to airway obstruction in the neonatal period. We present a case of epignathus immature teratoma with fetiform features, originating from basisphenoid in a 28-week preterm male baby, who succumbed to death immediately after birth. Since epignathus is a life-threatening condition at the time of delivery, a prenatal diagnosis is essential to coordinate the treatment and appropriate management by securing the airway, either by endotracheal intubation or tracheostomy followed by complete resection of the tumor.
上颌鼻型畸胎瘤是一种极为罕见的口咽畸胎瘤，通常起源于腭部，由于新生儿期气道阻塞导致高死亡率（80 - 100%）。我们报告一例具有胎儿样特征的上颌鼻型未成熟畸胎瘤病例，起源于一名28周早产男婴的蝶骨基部，该婴儿出生后即刻死亡。由于上颌鼻型畸胎瘤在分娩时是一种危及生命的疾病，产前诊断对于通过气管插管或气管切开确保气道安全，随后完整切除肿瘤来协调治疗和适当管理至关重要。
