Delmas M C, Bérard C
Service de rééducation fonctionnelle infantile l'Escale, centre hospitalier Lyon-Sud, Pierre-Bénite, France.
Pediatrie. 1990;45(7-8):457-64.
After a brief recall of clinical features, an outline of care for children with spinal muscular atrophy or severe neuromyopathies is proposed. With regard to respiration, the aim is to allow pulmonary growth, mainly through preventive ventilation. From the orthopaedic point of view, the main goal is to prevent contractures and kyphoscoliosis. Moreover, several methods of technical assistance can be proposed in order to make everyday life easier and allow familial and social insertion.
在简要回顾临床特征之后，本文提出了针对脊髓性肌萎缩症或严重神经肌肉病患儿的护理要点。在呼吸方面，目标主要是通过预防性通气来促进肺部发育。从骨科角度来看，主要目标是预防挛缩和脊柱侧弯。此外，可以提出几种技术辅助方法，以使日常生活更轻松，并促进患儿融入家庭和社会。
