Ogino T
Department of Physical Therapy, School of Allied Health Professions; Sapporo, Japan.
Hand Clin. 1990 Nov;6(4):661-71.
Definition, incidence, genetics, and etiology of typical cleft hand are discussed in this paper. Cleft hand, central polydactyly, and osseous syndactyly were induced experimentally when the same teratogenic factors acted on the embryos at the same developmental stage. Typical cleft hand, central polydactyly, and syndactyly should be classified together as manifestations of the same entity, that is, failure of induction of finger rays. Typical cleft hand may be further subdivided into five types on the basis of the number of defective finger rays. Treatment of the typical cleft hand involves cosmetic and functional considerations. Reduction of the wide interdigital space is performed primarily for cosmetic reasons, while separation of syndactyly between thumb and index finger and correction of deviation of the thumb is performed for functional improvement. A zigzag incision with a small triangular flap is recommended for reduction of the interdigital space. If metacarpal remnants or cross bones prevent drawing the metacarpals together, they should be removed. The deep transverse metacarpal ligament should be reconstructed by ligamentous flap made out of the flexor tendon sheaths of the index and ring fingers to prevent later spreading of the fingers. A dorsal-based rotation flap fashioned from the skin of the cleft is recommended for the treatment of cleft hand with partial syndactyly of the thumb and index finger. Deviation of the thumb is often caused by a delta phalanx by a trapezoidal-shaped extra phalanx. Deviation of the thumb is corrected by removing the delta phalanx or osteotomy of the trapezoidal phalanx. When the cleft is closed at approximately 1 year of age, spontaneous correction of the flexion deformity of the ring finger is sometimes observed.
本文讨论了典型裂手的定义、发病率、遗传学及病因。当相同的致畸因素在相同发育阶段作用于胚胎时,可实验性诱导出裂手、中央多指及骨性并指。典型裂手、中央多指及并指应归为同一实体的表现,即指射线诱导失败。典型裂手可根据缺陷指射线的数量进一步细分为五种类型。典型裂手的治疗涉及美观和功能方面的考虑。主要出于美观原因减少宽大的指间间隙,而分离拇指与示指之间的并指及矫正拇指偏斜则是为了改善功能。建议采用带有小三角皮瓣的锯齿状切口来减少指间间隙。如果掌骨残余或交叉骨妨碍将掌骨拉拢在一起,则应予以切除。应采用示指和环指指屈肌腱鞘制成的韧带瓣重建掌骨深横韧带,以防止手指日后散开。对于拇指与示指部分并指的裂手,建议采用由裂部皮肤形成的背侧旋转皮瓣进行治疗。拇指偏斜常由三角形指骨或梯形额外指骨引起。通过切除三角形指骨或对梯形指骨进行截骨来矫正拇指偏斜。当在大约1岁时闭合裂部时,有时可观察到环指屈曲畸形的自发矫正。