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临床病例研究:一名 4 岁男孩在切除髓母细胞瘤后出现后颅窝综合征。

Clinical case study: a 4-year-old boy with posterior fossa syndrome after resection of a medulloblastoma.

机构信息

Ohio State University, Columbus, OH, USA.

出版信息

J Neurosci Nurs. 2011 Aug;43(4):225-9. doi: 10.1097/JNN.0b013e3182212af9.

DOI:10.1097/JNN.0b013e3182212af9
PMID:21796045
Abstract

Posterior fossa syndrome can occur after neurosurgical resections of childhood posterior fossa tumors, such as medulloblastomas. Posterior fossa syndrome is characterized by transient mutism, emotional lability, cognitive deficits, weakness, ataxia, and cranial nerve dysfunction. Symptoms generally appear 1 to 3 days after surgery and persist for months to years. Neuroscience nurses play an integral role in helping affected children and their families through the diagnosis, treatment, and sequelae of this frightening syndrome.

摘要

后颅窝综合征可发生于儿童后颅窝肿瘤(如髓母细胞瘤)的神经外科切除术后。后颅窝综合征的特征为短暂性缄默症、情绪不稳、认知障碍、无力、共济失调和颅神经功能障碍。症状通常在手术后 1 至 3 天出现,并持续数月至数年。神经科学护士在帮助受影响的儿童及其家庭了解这一可怕综合征的诊断、治疗和后遗症方面发挥着不可或缺的作用。

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引用本文的文献

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Posterior fossa syndrome in children following tumor resection: Knowledge update.儿童肿瘤切除术后的后颅窝综合征:知识更新
Surg Neurol Int. 2016 Mar 11;7(Suppl 6):S179-83. doi: 10.4103/2152-7806.178572. eCollection 2016.
2
Cause and outcome of cerebellar mutism: evidence from a systematic review.小脑缄默症的病因与结局:一项系统评价的证据
Childs Nerv Syst. 2014 Mar;30(3):375-85. doi: 10.1007/s00381-014-2356-0. Epub 2014 Jan 23.