Uchida Yuto, Matsukawa Noriyuki, Oguri Takuya, Sakurai Keita, Miura Toshiyasu, Iwagaitsu Shiho, Naniwa Taio, Ojika Kosei
Department of Neurology, Nagoya City University, Japan.
Intern Med. 2011;50(15):1611-4. doi: 10.2169/internalmedicine.50.5185. Epub 2011 Aug 1.
We herein present the first reported case of reversible cerebral vasoconstriction syndrome (RCVS) in Takayasu's arteritis (TA), in a patient with severe thunderclap headache and generalized tonic-clonic seizure. Magnetic resonance imaging and angiography revealed posterior reversible encephalopathy syndrome, followed by severe vasoconstriction in multiple arteries. RCVS should be included in the differential diagnosis of thunderclap headache attacks with radiologic intracranial vascular abnormalities in connective tissue diseases, including TA.
我们在此报告首例Takayasu动脉炎（TA）合并可逆性脑血管收缩综合征（RCVS）的病例，患者表现为严重的霹雳样头痛和全身强直阵挛性发作。磁共振成像和血管造影显示为后部可逆性脑病综合征，随后多条动脉出现严重血管收缩。对于结缔组织病（包括TA）中伴有放射学颅内血管异常的霹雳样头痛发作，鉴别诊断时应考虑RCVS。
