右心房低度恶性子宫内膜间质肉瘤的囊性表现：病例报告

Wood Cristina L, Sederberg James, Russ Paul, Seres Tamas

Department of Anesthesiology, University of Colorado Hospital, 12631 E, 17th Avenue, Aurora, CO 80045, USA.

Cardiovasc Ultrasound. 2011 Aug 24;9:23. doi: 10.1186/1476-7120-9-23.

A 71-year-old woman presented with a right adnexal solid mass invading the right gonadal vein and inferior vena cava up to the hepatic veins revealed by CT and confirmed by MRI. A thin-walled cyst and a solid mass were unexpectedly found in the right atrium by transesophageal echocardiography (TEE) in the operating room. Using color Doppler and air bubbles as contrast material a circumscribed cyst was confirmed and localized close to the IVC. The cyst was connected to the mass in the inferior vena cava. The tumor, including the cyst, was removed without using cardiopulmonary bypass and described as a low-grade endometrial stromal sarcoma, a rare slowly growing tumor. This is the first TEE description of endometrial stromal sarcoma manifesting as a right atrial cyst.

一名71岁女性因右附件实性肿块就诊，CT显示该肿块侵犯右性腺静脉及下腔静脉直至肝静脉，MRI予以证实。术中经食管超声心动图（TEE）意外发现右心房有一个薄壁囊肿和一个实性肿块。使用彩色多普勒并以气泡作为对比剂，确认了一个边界清晰的囊肿，并定位其靠近下腔静脉。该囊肿与下腔静脉内的肿块相连。未使用体外循环就切除了包括囊肿在内的肿瘤，病理诊断为低级别子宫内膜间质肉瘤，这是一种罕见的生长缓慢的肿瘤。这是首次通过TEE描述表现为右心房囊肿的子宫内膜间质肉瘤。