Iba Ba Josaphat, Nzenze Jean Raymond, Moubamba Franck, Mboumba Angela Sonia Iroki, Missounga Landry, Bignoumba Ibouili Rufin, Coniquet Sophie, Moussavou Kombila Jean-Baptiste, Boguikouma Jean Bruno
Centre hospitalier de Libreville, Service de médecine A, BP 2228 Libreville, Gabon.
Sante. 2011 Apr-Jun;21(2):97-101. doi: 10.1684/san.2011.0241.
Still disease is an inflammatory rheumatism occurring predominantly in children and adolescents, but which is sometimes diagnosed in adults. A combination of fever, arthralgia, transient dermatological lesions, hyperleucocytosis predominantly neutrophilic, and ferritinaemia greater than 1,000 μg/L is suggestive of this disease, but infectious, haematological, immunological, and tumor diseases must first be ruled out. Accordingly, patients' financial limitations keep this disease from being diagnosed often in sub-Saharan Africa. We report four cases of Still disease with favourable outcome after corticosteroid therapy.
斯蒂尔病是一种主要发生在儿童和青少年中的炎性风湿病，但有时也在成人中被诊断出来。发热、关节痛、短暂性皮肤病变、以中性粒细胞为主的白细胞增多症以及铁蛋白血症大于1000μg/L的组合提示该病，但必须首先排除感染性、血液学、免疫学和肿瘤性疾病。因此，患者的经济限制使得这种疾病在撒哈拉以南非洲地区常常无法得到诊断。我们报告了4例斯蒂尔病患者，经皮质类固醇治疗后预后良好。
