Stöberl C, Partsch H
Dermatologische Abteilung der KA Rudolfstiftung, Wien.
Z Hautkr. 1990 Feb;65(2):139-42, 145-6.
Primary lymphedema of the lower extremities is a clinical entity often misdiagnosed, especially in its mild, distal forms. Its characteristics are: swelling, tightness of the skin, and deepening of the skin folds of one foot, mainly in young girls. Proximal forms with involvement of the lower leg and thigh are often congenital. In later years, these manifestations have to be distinguished from secondary lymphedema due to a block in the lymph nodes (e.g. in malignoma), starting with swelling of the proximal regions of the extremities and the genitalia. Indirect lymphography, especially with new contrast media, however, offer new diagnostic possibilities. The best routine method to confirm or exclude lymphedema is isotopic lymphography.
下肢原发性淋巴水肿是一种常被误诊的临床病症，尤其是在其轻度、远端型时。其特征为：肿胀、皮肤紧绷以及单足皮肤褶皱加深，主要见于年轻女孩。累及小腿和大腿的近端型通常为先天性。数年后，这些表现必须与因淋巴结阻塞（如恶性肿瘤）导致的继发性淋巴水肿相鉴别，后者始于四肢近端及生殖器部位的肿胀。然而，间接淋巴造影，尤其是使用新型造影剂时，提供了新的诊断可能性。确认或排除淋巴水肿的最佳常规方法是同位素淋巴造影。
