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婴儿期后完全性肺静脉异位连接

Total anomalous pulmonary venous connection beyond infancy.

作者信息

Reddy Kandakure Pramod, Nagarajan Ramodass, Rani Usha, Prasad Shiva, Chakravarthy Srinivas, Rao Ivatury M, Murthy Kona Samba

机构信息

Innova Children's Heart Hospital, Tarnaka, Hyderabad, India.

出版信息

Asian Cardiovasc Thorac Ann. 2011 Jun;19(3-4):249-52. doi: 10.1177/0218492311409570.

DOI:10.1177/0218492311409570
PMID:21885551
Abstract

Most patients with total anomalous pulmonary venous connection are operated on in infancy, with low mortality and morbidity, but in developing countries, we still encounter patients beyond infancy. We describe our experience in 26 patients aged 1-16 years (mean, 5.01 years), with total anomalous pulmonary venous connection, who underwent correction between June 2007 and December 2009. Eleven patients were >5-years old. Transthoracic echocardiography was diagnostic in all cases. Mean intensive care unit stay was 2.3 ± 0.87 days, and hospital stay was 9.23 ± 2.34 days. There were no early deaths and no major postoperative complications. Follow-up ranged from 10-40 months. Pulmonary artery pressure, as judged by echocardiography, reduced significantly in all patients. Repair of total anomalous pulmonary venous connection beyond infancy can be carried out safely with acceptable results.

摘要

大多数完全性肺静脉异位连接患者在婴儿期接受手术,死亡率和发病率较低,但在发展中国家,我们仍会遇到超过婴儿期的患者。我们描述了2007年6月至2009年12月期间接受矫正手术的26例年龄在1至16岁(平均5.01岁)的完全性肺静脉异位连接患者的经验。11例患者年龄大于5岁。所有病例经胸超声心动图均能明确诊断。平均重症监护病房停留时间为2.3±0.87天,住院时间为9.23±2.34天。无早期死亡病例,也无重大术后并发症。随访时间为10至40个月。经超声心动图判断,所有患者的肺动脉压力均显著降低。婴儿期后完全性肺静脉异位连接的修复手术可以安全进行,效果良好。

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1
Total anomalous pulmonary venous connection beyond infancy.婴儿期后完全性肺静脉异位连接
Asian Cardiovasc Thorac Ann. 2011 Jun;19(3-4):249-52. doi: 10.1177/0218492311409570.
2
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Rev Port Cir Cardiotorac Vasc. 2012 Jan-Mar;19(1):11-6.
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Repair of total anomalous pulmonary venous connection in early infancy.婴儿早期完全性肺静脉异位连接的修复
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Repair of total anomalous pulmonary venous connection in infancy: experience from a developing country.婴儿期完全性肺静脉异位连接的修复:来自一个发展中国家的经验。
Ann Thorac Surg. 1999 Jul;68(1):155-9. doi: 10.1016/s0003-4975(99)00375-6.
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Long-term results after repair of total anomalous pulmonary venous connection.完全性肺静脉异位连接修复术后的长期结果。
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