Terakawa Yuzo, Tsuyuguchi Naohiro, Takami Toshihiro, Ohata Kenji
Department of Neurosurgery, Osaka City University Graduate School of Medicine, Osaka, Japan.
J Korean Neurosurg Soc. 2011 Jul;50(1):51-3. doi: 10.3340/jkns.2011.50.1.51. Epub 2011 Jul 31.
We present a rare case of medulloblastoma which presented with unilateral sudden sensorineural hearing loss as an initial symptom. A 19-year-old man was admitted to our hospital with a chief complaint of dizziness and facial numbness on the right side. His illness had begun two years previously with sudden hearing loss on the right side, for which he had been treated as an idiopathic sudden hearing loss. Magnetic resonance imaging demonstrated abnormal signals located mainly in the right middle cerebellar peduncle. We performed partial resection of the tumor by suboccipital craniotomy. The histopathological diagnosis was medulloblastoma. Intrinsic brain tumor is an extremely rare cause of sudden sensorineural hearing loss and is therefore easily overlooked as was in the present case. The present case highlights not only the need to evaluate patients with sudden sensorineural hearing loss by magnetic resonance imaging but also the importance of paying attention to intrinsic lesions involving the brainstem. Although this condition like the presented case might be rare, intrinsic brain tumor should be considered as a potential cause of sudden sensorineural hearing loss, as it may be easily missed leading to a delay in appropriate treatment.
我们报告一例罕见的髓母细胞瘤，其最初症状为单侧突发感音神经性听力损失。一名19岁男性因右侧头晕和面部麻木为主诉入院。他的病情始于两年前右侧突发听力损失，当时被当作特发性突发听力损失进行治疗。磁共振成像显示异常信号主要位于右侧小脑中脚。我们通过枕下开颅术对肿瘤进行了部分切除。组织病理学诊断为髓母细胞瘤。原发性脑肿瘤是突发感音神经性听力损失极为罕见的病因，因此在本例中很容易被忽视。本例不仅凸显了对突发感音神经性听力损失患者进行磁共振成像评估的必要性，还强调了关注累及脑干的原发性病变的重要性。尽管像本例这样的情况可能很罕见，但原发性脑肿瘤应被视为突发感音神经性听力损失的潜在病因，因为它可能很容易被漏诊，从而导致适当治疗的延误。
