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两例孤立性永存左上腔静脉伴右上腔静脉缺如。

Isolated persistent left superior vena cava with absent right superior vena cava in two cases.

作者信息

Korkmaz Levent, Akyüz Ali Rıza, Erkuş M Emre, Topal Cevat

机构信息

Department of Cardiology, Ahi Evren Chest, Heart and Vascular Surgery Training and Research Hospital, Trabzon, Turkey.

出版信息

Turk Kardiyol Dern Ars. 2011 Sep;39(6):501-4. doi: 10.5543/tkda.2011.01453.

Abstract

Persistent left superior vena cava (LSVC) with absent right superior vena cava (RSVC) is a very rare congenital anomaly. Its isolated existence is even rarer. Persistent LSVC is usually asymptomatic and discovered incidentally. We present persistent LSVC with absent RSVC in two asymptomatic patients, namely, a 52-year-old woman and 65-year-old man. The diagnosis was confirmed by cardiac computed tomography in both cases.

摘要

永存左上腔静脉(LSVC)伴右上腔静脉(RSVC)缺如是一种非常罕见的先天性异常。其单独存在更为罕见。永存LSVC通常无症状,多为偶然发现。我们报告了两例无症状患者,分别为一名52岁女性和一名65岁男性,均为永存LSVC伴RSVC缺如。两例均经心脏计算机断层扫描确诊。

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