Odemis Ender, Akdeniz Celal, Saygili Ozlem Barutcu, Karaci Ali Riza
Department of Pediatric Cardiology, Istanbul Mehmet Akif Ersoy, Thoracic and Cardiovascular Surgery Center and Research Hospital, Istanbul, Turkey.
Ann Pediatr Cardiol. 2011 Jul;4(2):183-5. doi: 10.4103/0974-2069.84667.
Levoatriocardinal vein (LACV) is characterized by an abnormal connection between pulmonary and systemic venous return. This extremely rare cardiac malformation is usually associated with left-sided obstructive lesions including mitral atresia, hypoplastic left-heart syndrome, and abnormal pulmonary venous connection. Patients may have low systemic cardiac output and pulmonary venous obstruction symptoms. In this manuscript, we report a case with LACV and normal pulmonary venous return with absence of any intracardiac pathology. LACV was demonstrated with echocardiography, angiography, and computed tomography. Surgical correction was made successfully.
左心房静脉（LACV）的特征是肺静脉回流与体静脉回流之间存在异常连接。这种极其罕见的心脏畸形通常与左侧阻塞性病变相关，包括二尖瓣闭锁、左心发育不全综合征和异常肺静脉连接。患者可能出现低心输出量和肺静脉阻塞症状。在本手稿中，我们报告了一例LACV且肺静脉回流正常且无任何心内病变的病例。通过超声心动图、血管造影和计算机断层扫描证实了LACV。手术矫正成功完成。
