Pawelec-Wojtalik Malgorzata, Iorio Fiore S, Anwar Ashraf M, El Midany Ashraf A H
Department of Pediatric Cardiology, University of Medical Sciences, Poznan, Poland.
Interact Cardiovasc Thorac Surg. 2011 Dec;13(6):669-71. doi: 10.1510/icvts.2011.277491. Epub 2011 Oct 6.
Congenital mitral ring is a rare type of congenital mitral stenosis. There are two types of mitral ring: the intramitral ring and the supramitral ring. Intramitral rings are often associated with complex valve pathology, and therefore have a worse prognosis than supramitral rings, in which the mitral apparatus is usually normal. The role of echocardiography in the evaluation of the mitral valve apparatus is crucial, because it allows an identification of the types of malformation, their hemodynamic repercussion and early predictors of the outcome. We describe two cases of intramitral ring, the diagnostic challenge they provided, and the value of the information obtained using real-time three-dimensional echocardiography in such cases.
先天性二尖瓣环是一种罕见的先天性二尖瓣狭窄类型。二尖瓣环有两种类型：二尖瓣内环和二尖瓣上环。二尖瓣内环常与复杂的瓣膜病变相关，因此预后比二尖瓣上环更差，二尖瓣上环的二尖瓣装置通常正常。超声心动图在评估二尖瓣装置中的作用至关重要，因为它能够识别畸形类型、其血流动力学影响以及结局的早期预测因素。我们描述了两例二尖瓣内环病例、它们带来的诊断挑战以及在此类病例中使用实时三维超声心动图获得的信息的价值。
