[半侧肥大和脊柱侧弯提示合并脊髓空洞症的Chiari 1畸形]

[Hemihypertrophy and scoliosis revealing a Chiari 1 malformation with syringomyelia].

作者信息

Benjamin M-D, Santiago J, Hebert J-C, Thirion S, Ranaivojaona S, Alvarez C, Atallah A, Sibille G, Bataille H, Porlys M, Ebrad P

机构信息

Service de pédiatrie, centre hospitalier de Basse-Terre, avenue Gaston-Feuillard, 97109 Basse-Terre, Guadeloupe.

出版信息

Arch Pediatr. 2011 Nov;18(11):1210-5. doi: 10.1016/j.arcped.2011.08.022. Epub 2011 Oct 5.

DOI:10.1016/j.arcped.2011.08.022

PMID:21982271

Abstract

We report the case of a 9-year-old boy with progressive thoracic scoliosis and crossed hemihypertrophy who was discovered with a Chiari 1 malformation and syringomyelia. These disorders are connected by complex physiopathological mechanisms; their association deserves attention. This observation reviews the importance of the clinical examination, particularly the neurological exam, in childhood scoliosis. The features suggesting a neurogenic background of spine deformation should be sought. Scoliosis with hemihypertrophy can be the sign of an underlying neurological abnormality.

摘要

我们报告了一例9岁男孩的病例，该男孩患有进行性胸椎侧弯和交叉性半身肥大，同时被发现患有Chiari 1畸形和脊髓空洞症。这些病症通过复杂的生理病理机制相互关联；它们的关联值得关注。本病例回顾了临床检查，尤其是神经系统检查在儿童脊柱侧弯中的重要性。应寻找提示脊柱变形具有神经源性背景的特征。伴有半身肥大的脊柱侧弯可能是潜在神经异常的迹象。