[Petrous apex cephalocele is a rare disease].

Petrous apex cephalocele (PAC) is a rare lesion, which represents a herniation from the posteriolateral portion of Meckel's cave into the petrous apex. The pathologic explanation is still unknown. We report a patient with clinical symptoms of facial pain, hearing loss and cerebrospinal fluid otorrhea. A computertomography and a magnetic resonance scan revealed that the symptoms were caused by PAC. The patient was later successfully operated by means of middle fossa approach.