Khaled A, Kourda M, Fazaa B, Kourda J, Ben Jilani S, Kamoun M Ridha, Zermani R
Department of Dermatology, Charles Nicolle Hospital, Tunis, Tunisia.
Pathologica. 2011 Jun;103(3):73-6.
Malignant proliferating trichilemmal cyst is a rare tumour usually located on the scalp of elderly women. About 40 cases of malignant proliferating trichilemmal tumour have been documented.
We report a case of a malignant proliferating trichilemmal cyst of the scalp in a 57-year-old woman. On the vertex she had a voluminous vegetated and multinodular tumour measuring 7 x 5 cm with spontaneous and abundant bleeding, and another lesion of the scalp corresponding to a trichilemmal cyst. Based on histopathological findings, the case was diagnosed as malignant proliferating trichilemmal cyst.
Diagnostic, clinicoprognostic and histological features of this tumour are discussed. Treatment is not yet standardized given its rarity.
恶性增生性外毛根鞘囊肿是一种罕见肿瘤,通常位于老年女性头皮。已记录约40例恶性增生性外毛根鞘肿瘤。
我们报告一例57岁女性头皮恶性增生性外毛根鞘囊肿。在头顶她有一个巨大的、呈息肉状且多结节的肿瘤,大小为7×5厘米,有自发且大量出血,头皮还有另一处病变,为外毛根鞘囊肿。根据组织病理学检查结果,该病例被诊断为恶性增生性外毛根鞘囊肿。
讨论了该肿瘤的诊断、临床预后及组织学特征。鉴于其罕见性,治疗尚未标准化。