Wang Yi-Min, Chuang Ming-Jung, Cheng Min-Hsiung
Department of Neurosurgery, Chang Gung University College of Medicine, Kaohsiung, Taiwan.
Acta Neurol Taiwan. 2011 Sep;20(3):188-91.
Congenital dermal sinus tract (DST), an uncommon entity of cranial or spinal dysraphism, occurs along the midline neuraxis that may arise from nasion and occiput down to the lumbar and sacral region. It is often diagnosed in infants and children for skin signs, neurological deficits, local infection, meningitis, or abscess. For spinal DST, there is a paucity of case or series report in Taiwan.
In this paper, we report a case in a 6-year-old girl. The girl presented with midline lumbar skin dimple, hypertrichosis, and history of bacterial meningitis. She was successful treated by surgical excision of the DST with local infection that ended within the subarachnoid space between L2-3 vertebrae.
This case highlights the importance of a thorough examination of the midline craniospinal axis in children with meningitis or history of meningitis.
先天性真皮窦道（DST）是一种罕见的颅或脊柱神经管闭合不全疾病，沿中线神经轴发生，可起自鼻根和枕部，向下延伸至腰骶部。它常在婴幼儿和儿童期因皮肤体征、神经功能缺损、局部感染、脑膜炎或脓肿而被诊断。对于脊髓DST，台湾地区的病例或系列报道较少。
本文报告一名6岁女孩的病例。该女孩表现为腰部中线皮肤凹陷、多毛症以及细菌性脑膜炎病史。通过手术切除终止于L2 - 3椎体蛛网膜下腔的伴有局部感染的DST，她得到了成功治疗。
该病例强调了对患有脑膜炎或有脑膜炎病史的儿童进行颅脊柱中轴线全面检查的重要性。
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