三发性腰椎皮样窦道：一种典型的孤立性中线病变的不寻常表现。
Triple lumbar dermal sinuses: unusual presentation of a typically solitary midline lesion.
作者信息
Ansari Saeed, Andrabi Yasir, El Khashab Mostafa, Bateni Farzad, Dadmehr Majid, Iskandar Bermans J, Nejat Farideh
机构信息
Department of Neurosurgery, Children's Hospital Medical Center, Tehran University of Medical Science, Tehran, Iran.
出版信息
Pediatr Neurosurg. 2009;45(4):305-7. doi: 10.1159/000235605. Epub 2009 Aug 19.
BACKGROUND
Congenital dermal sinus is a type of closed spinal dysraphism caused by incomplete disjunction. The lesion occurs everywhere along neuraxis predominantly as a solitary midline sinus in the lumbosacral area.
CASE HISTORY
The authors report on a 10-month-old girl with triple congenital dermal sinuses associated with dermoid tumors and intradural extension of one of them.
DISCUSSION
Triple dermal sinuses of the lumbosacral area in a single patient have never been described previously. Incomplete disjunction is suggested to cause this abnormality thereafter the orifice may be divided to three sinuses and some mesenchymal tissues separated the two proximal sinuses to a paramedian location.
背景
先天性皮样窦是一种由不完全分离引起的闭合性脊柱裂。该病变沿神经轴在任何部位均可发生，主要表现为腰骶部孤立的中线窦。
病例报告
作者报道了一名10个月大的女孩，患有三处先天性皮样窦，伴有皮样囊肿，其中一处向硬膜内延伸。
讨论
此前从未有过关于单一患者腰骶部三处皮样窦的描述。提示不完全分离导致了这种异常，此后窦口可能分为三个窦，一些间充质组织将两个近端窦分隔至旁正中位置。
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