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儿童Castleman 病:三例报告并文献复习。

Castleman's disease in childhood: report of three cases and review of the literature.

机构信息

Unit of Pediatric Hematology and Oncology, G Di Cristina Children's Hospital, ARNAS, Palermo, Italy.

出版信息

Ital J Pediatr. 2011 Oct 20;37:50. doi: 10.1186/1824-7288-37-50.

Abstract

Castleman's disease (CD) is a rare, localized or generalized, lymphoproliferative disorder with a frequent mediastinal location, but possible in any lymph node or extra nodal site. It usually appears in young adults whilst it rarely occurs in childhood. There are only about 100 pediatric cases published, five of them in Italy. We report 3 cases of localized Castleman's disease, investigated in our Department in a 3 years period and reviewed the literature.

摘要

血管滤泡性淋巴结增生症(CD)是一种罕见的局限性或全身性淋巴组织增生性疾病,常发生于纵隔,但也可能发生于任何淋巴结或淋巴结外部位。它通常发生于年轻人,而在儿童中很少见。目前仅有约 100 例儿科病例报道,其中 5 例发生在意大利。我们报告了 3 例局限性血管滤泡性淋巴结增生症病例,这些病例是在我们科室 3 年期间进行调查的,并对文献进行了回顾。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7979/3219574/999365f98e6f/1824-7288-37-50-1.jpg

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