Deb Subrato J
Thoracic Surgical Services, Western Maryland Regional Medical Center, 12502 Willowbrook Road, Suite 470, Cumberland, Maryland 21502, USA.
J Med Case Rep. 2011 Oct 21;5:519. doi: 10.1186/1752-1947-5-519.
In this report, the case of an adult patient with a massive right-sided Bochdalek hernia with multiple displaced abdominal organs, including the liver and gallbladder, is described. This patient presented with acute cholecystitis of the malpositioned gallbladder. During surgery, nodular regenerative hyperplasia of the liver was also found. To the best of this author's knowledge, these two entities have never been reported in association with this rare condition.
A 54-year-old Caucasian man presented with nausea and epigastric pain. He had a known history of right-sided Bochdalek hernia which was being managed expectantly. A computerized tomogram revealed the massive hernia with displaced stomach, liver, intestine and omentum into his right thorax. It was believed that our patient had bowel incarceration and he was therefore taken to surgery, where acute cholecystitis and a macronodular liver was identified. A thoracoabdominal approach was used to remove his gallbladder, reduce the herniated viscera and reconstruct his diaphragm. A liver biopsy identified nodular regenerative hyperplasia of the ectopic liver. There were no postoperative complications and at 12 month follow-up, our patient continues to do well.
This case report describes two unusual findings associated with a congenital Bochdalek diaphragmatic hernia that have never been reported. In addition, unique caveats to the surgical management of this complex rare condition are discussed.
在本报告中,描述了一例成年患者,患有巨大的右侧博赫dalek疝,伴有多个移位的腹部器官,包括肝脏和胆囊。该患者出现了异位胆囊的急性胆囊炎。在手术过程中,还发现了肝脏的结节性再生性增生。据作者所知,这两种情况从未与这种罕见疾病相关联地被报道过。
一名54岁的白种男性出现恶心和上腹部疼痛。他有右侧博赫dalek疝的已知病史,此前一直采取保守治疗。计算机断层扫描显示巨大疝,胃、肝脏、肠道和网膜移位至其右胸腔。据信我们的患者存在肠管嵌顿,因此被送往手术室,术中发现急性胆囊炎和肝脏大结节。采用胸腹联合入路切除胆囊,还纳疝出的内脏并重建膈肌。肝脏活检确定异位肝脏存在结节性再生性增生。术后无并发症,在12个月的随访中,我们的患者情况良好。
本病例报告描述了与先天性博赫dalek膈肌疝相关的两个异常发现,此前从未有过报道。此外,还讨论了这种复杂罕见疾病手术治疗的独特注意事项。