Layangool Thanarat, Promphan Worakan, Kirawittaya Tawatchai, Sangtawesin Chaisit, Makarapong Perapat
Cardiology Unit, Queen Sirikit National Institute of Child Health, College of Medicine, Rangsit University, Bangkok, Thailand.
J Med Assoc Thai. 2011 Aug;94 Suppl 3:S217-21.
To report 2 cases of severe combined aortic and pulmonic valvular stenosis.
To find patients with a diagnosis of severe combined aortic and pulmonic valvular stenosis, the authors searched in the patient profile at the cardiology unit, Queen Sirikit National Institute of Child Health (QSNICH) from 1995 to 2010.
There are 2 cases of severe combined aortic and pulmonic valvular stenosis from 19,416 case records of pediatric cardiac patients. The first one is a 9-year-old girl and the other is a male neonate. The interval between the presentations of these two cases was 10 years. The older patient, who had associated moderate aortic regurgitation, underwent aortic root replacement and pulmonic valvulotomy in the year 2000. The neonate, who presented in 2010 had undergone bilateral percutaneous balloon aortic and pulmonic valvuloplasty and required repeated balloon aortic valvuloplasty at the age of two months. Both patients responded well to treatment and were asymptomatic at the last follow-up of 10 years and 6 months respectively after treatment.
Combined aortic and pulmonic valvular stenosis is a very rare congenital heart disease. The prevalence is 0.01% of congenital heart disease at QSNICH. Bilateral balloon valvuloplasty of aortic and pulmonic valve is effectively performed in this rare congenital heart disease and can be done safely in a sick neonate.
