Department of Pediatric Urology, Pediatric Surgery Service, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS, Brazil.
J Pediatr Surg. 2011 Nov;46(11):2184-6. doi: 10.1016/j.jpedsurg.2011.08.022.
We describe a unique association of congenital rectourethral fistula with long tubular duplication of the colon in a boy with Klippel-Feil syndrome and Sprengel deformity. He presented with a rectourethral fistula after surgical repair of a tubular duplication of the terminal ileum, colon, and proximal rectum. Preoperative identification of the fistula was challenging and was only achieved after cystoscopy with injection of methylene blue under pressure through Foley catheters placed into the anus and distal stoma of a colostomy. Surgical repair was performed through the posterior sagittal approach. The patient is doing well after 4 years of follow-up.
我们描述了一例具有 Klippel-Feil 综合征和 Sprengel 畸形的男孩，其存在先天性直肠尿道瘘与结肠长管状重复畸形的独特关联。他在接受末端回肠、结肠和近端直肠的管状重复畸形的手术修复后出现直肠尿道瘘。瘘管的术前识别具有挑战性，仅在通过肛门和结肠造口术远端造口插入的 Foley 导管经膀胱镜检查加压注射亚甲蓝后才得以实现。手术修复通过后路矢状入路进行。患者在随访 4 年后恢复良好。
