Center for Experimental Medicine, the Third Xiangya Hospital, Central South University, Changsha, China.
Am J Med Genet B Neuropsychiatr Genet. 2012 Jan;159B(1):72-6. doi: 10.1002/ajmg.b.32003. Epub 2011 Nov 16.
Tourette Syndrome (TS) is a complex neuropsychiatric disorder characterized by vocal and motor tics. While environmental causes have been proposed to play a role, genetic factors are believed to be the main determinants of the disorder and its clinical manifestations. Recently, a heterozygous W317X mutation in the histidine decarboxylase gene (HDC) was reported to be responsible for TS in a two-generation pedigree. To investigate whether the HDC gene play a role in TS in Chinese Han population, we performed genetic analysis of the coding region of the HDC gene in 100 Chinese Han patients with TS. Three variants were found including a C > T transition (IVS1 + 52C > T), a novel C > A transition (c.426C > A) in exon 4, and a novel G > A transition (c.1743G > A) in exon 12, both predicted with no amino acid change. Extended analysis was conducted in a total of 120 TS patients and 240 sex, age, and ethnicity matched healthy controls. No significant differences in genotypic and allele distribution between patients and controls for these three variants (P = 0.274, P = 1.000 and P = 0.632 for genotypic distribution, respectively; P = 0.143, P = 1.000 and P = 0.582 for allele distribution, respectively) were observed, suggesting variants in the HDC gene may play little or no role in TS susceptibility in Chinese Han population.
妥瑞氏症(TS)是一种复杂的神经精神疾病,其特征为发声和运动抽搐。虽然已经提出环境因素可能起作用,但遗传因素被认为是该疾病及其临床表现的主要决定因素。最近,报道在一个两代家系中,组氨酸脱羧酶基因(HDC)的杂合 W317X 突变是导致 TS 的原因。为了研究 HDC 基因是否在汉族人群中与 TS 相关,我们对 100 例汉族 TS 患者的 HDC 基因编码区进行了遗传分析。发现了三个变异,包括一个 C>T 转换(IVS1+52C>T)、一个新的 C>A 转换(c.426C>A)在 4 号外显子和一个新的 G>A 转换(c.1743G>A)在 12 号外显子,均预测无氨基酸改变。在总共 120 例 TS 患者和 240 例性别、年龄和种族匹配的健康对照者中进行了扩展分析。这些三个变异的基因型和等位基因分布在患者和对照组之间没有显著差异(P=0.274、P=1.000 和 P=0.632 分别为基因型分布;P=0.143、P=1.000 和 P=0.582 分别为等位基因分布),提示 HDC 基因的变异在汉族人群中对 TS 的易感性可能作用不大或没有作用。