Watanabe K, Yamamoto N, Negoro T, Takahashi I, Aso K, Maehara M
Department of Pediatrics, Nagoya University School of Medicine, Japan.
J Clin Neurophysiol. 1990 Jul;7(3):409-16. doi: 10.1097/00004691-199007000-00006.
Benign infantile epilepsy with complex partial seizures is characterized by a high incidence of family history of benign childhood convulsions, normal development prior to onset, infantile onset, no underlying disorders, no neurological abnormalities, normal interictal EEGs, good response to treatment, and complete remission with normal developmental outcome. Seizures often occur in clusters, consisting of motion arrest, decreased responsiveness, staring or blank eyes mostly with simple automatisms, and mild convulsive movements associated with focal paroxysmal discharges, most frequently in the temporal area.
伴有复杂部分性发作的良性婴儿癫痫的特征为良性儿童惊厥家族史发生率高、发作前发育正常、婴儿期起病、无潜在疾病、无神经学异常、发作间期脑电图正常、对治疗反应良好以及完全缓解且发育结局正常。发作常成串出现,包括动作停止、反应性降低、凝视或目光呆滞,大多伴有简单自动症,以及与局灶性阵发放电相关的轻度惊厥运动,最常见于颞区。