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过敏性紫癜合并后脑可逆性脑病综合征。

Henoch-Schönlein purpura with posterior reversible encephalopathy syndrome.

机构信息

Department of Paediatric Neurology, Newcastle upon Tyne Hospitals National Health Service Foundation Trust, Newcastle upon Tyne, UK.

出版信息

Pediatr Neurol. 2012 Jan;46(1):42-3. doi: 10.1016/j.pediatrneurol.2011.10.006.

DOI:10.1016/j.pediatrneurol.2011.10.006
PMID:22196491
Abstract

We describe atypical Henoch-Schönlein purpura with posterior reversible encephalopathy syndrome in a normotensive 11-year-old girl. Her Henoch-Schönlein purpura was atypical because she initially presented with abdominal pain and vomiting and neurologic complications, rather than with the classic rash of Henoch-Schönlein Purpura. This previously healthy child was also unusual because she manifested the radiologic and clinical features of posterior reversible encephalopathy syndrome in the absence of hypertension induced by Henoch-Schönlein purpura. Her abnormal findings resolved with supportive therapy. We discuss the association of posterior reversible encephalopathy syndrome with Henoch-Schönlein purpura in three previously reported cases.

摘要

我们描述了一例非典型过敏性紫癜合并后部可逆性脑病综合征的病例,患者为 11 岁的血压正常女孩。她的过敏性紫癜是非典型的,因为她最初表现为腹痛、呕吐和神经系统并发症,而不是典型的过敏性紫癜皮疹。这位既往健康的儿童也很不寻常,因为她在没有由过敏性紫癜引起的高血压的情况下表现出了后部可逆性脑病综合征的放射学和临床特征。她的异常表现通过支持性治疗得到了缓解。我们讨论了后部可逆性脑病综合征与过敏性紫癜在三个已报道病例中的关联。

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