Nofuentes Riera Carmen, Mella Laborde Mario, Pérez Bru Susana, Soliveres Soliveres Edelmira, Hernández Quiles Antonio, García García Salvador
Servicio de Cirurgía Generaly del Aparato Digestivo, Hospital Universitario San Juan de Alicante, Alicante, España.
Acta Gastroenterol Latinoam. 2011 Sep;41(3):238-41.
Leiomyomatosis peritonealis disseminata (LPD) is a rare, benign proliferative process characterized by multiple smooth muscle nodules throughout the peritoneum. Predominantly affects women in their reproductive years. The cause of LPD is unknown although it may be associated with high estrogen state. The clinical appearance mimics a peritoneal carcinomatosis and the radiologic findings are unspecific. So, the definitive diagnosis is histological. Treatment must be individualized depending on age, hormonal status and symptomatology. To date, less than 140 cases have been reported. We report a case of LPD in a 50-year-old woman presented as an intestinal obstruction.
播散性腹膜平滑肌瘤病（LPD）是一种罕见的良性增殖性疾病，其特征是整个腹膜出现多个平滑肌结节。主要影响育龄期女性。LPD的病因尚不清楚，尽管可能与高雌激素状态有关。临床表现类似腹膜癌，影像学表现不具特异性。因此，确诊需依靠组织学检查。治疗必须根据年龄、激素状态和症状进行个体化。迄今为止，报道的病例不足140例。我们报告一例50岁女性LPD患者，表现为肠梗阻。
