肺肿瘤性血栓性微血管病伴肺心病，源于促纤维增生性小圆细胞肿瘤。

Pulmonary tumor thrombotic microangiopathy with cor pulmonale due to desmoplastic small round cell tumor.

机构信息

Department of Pathology, Robert Wood Johnson Medical School, New Brunswick, NJ 08903, USA.

出版信息

J Pediatr. 2012 Apr;160(4):697-9. doi: 10.1016/j.jpeds.2011.12.010. Epub 2012 Jan 10.

DOI:10.1016/j.jpeds.2011.12.010

Abstract

A 12-year-old boy presented acutely after an episode of syncope with perioral cyanosis. He died 19 hours after admission due to cor pulmonale as a complication of metastatic desmoplastic small round cell tumor in the lungs with associated tumor thrombotic microangiopathy.

摘要

一名 12 岁男孩在晕厥发作后出现口唇周围发绀，随后紧急送医。入院 19 小时后，他因肺转移性促纤维增生性小圆细胞肿瘤合并肿瘤血栓性微血管病导致的肺心病去世。