胎儿颅咽管瘤：一例早期经子宫 EXIT（子宫内产时治疗）病例。
Fetal epignathus: the case of an early EXIT (ex utero intrapartum treatment).
机构信息
From the Department of Obstetrics and Gynecology, University of California, Irvine, Orange, California.
出版信息
Obstet Gynecol. 2012 Feb;119(2 Pt 2):466-470. doi: 10.1097/AOG.0b013e318242b3f1.
BACKGROUND
Fetal epignathus, a teratoma arising from the oropharynx that may be lethal, can be diagnosed prenatally.
CASE
A 29-year-old woman, gravida 1, was evaluated for an elevated alpha-fetoprotein level. Imaging evaluation revealed a fetal epignathus without intracranial extension. Preterm labor necessitated delivery at 27 5/7 weeks of gestation with ex utero intrapartum treatment (EXIT) procedure using a classical incision. The neonate's small size and short umbilical cord required complete exteriorization to secure the airway. Pathology revealed an immature teratoma.
CONCLUSION
Prenatal diagnosis of fetal epignathus is imperative so that all options can be discussed. An EXIT procedure may be necessary for airway management at birth. If preterm delivery is necessary, choice of uterine incision and fetal size are important factors to consider for a successful outcome.
背景
胎儿颅咽管瘤是一种源自口咽的畸胎瘤，可能致命，可在产前诊断。
病例
一位 29 岁的初产妇，因甲胎蛋白水平升高而接受评估。影像学评估显示胎儿颅咽管瘤无颅内延伸。早产导致妊娠 27 周+5 天分娩，采用经典切口行宫外产时处理（EXIT）手术。新生儿体型小且脐带短，需要完全外置以确保气道通畅。病理检查显示为未成熟畸胎瘤。
结论
产前诊断胎儿颅咽管瘤至关重要，以便讨论所有选择。在出生时可能需要 EXIT 手术来进行气道管理。如果需要早产，子宫切口的选择和胎儿大小是成功分娩的重要考虑因素。
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