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接受异基因干细胞移植治疗的儿童原始浆细胞样树突状细胞肿瘤

Childhood blastic plasmacytoid dendritic cell neoplasm treated with allogenic stem cell transplantation.

作者信息

Gambichler Thilo, Pantelaki Ioanna, Stücker Markus

机构信息

Department of Dermatology, Ruhr-University Bochum, Bochum, Germany.

出版信息

Pediatr Dermatol. 2013 Jan-Feb;30(1):142-4. doi: 10.1111/j.1525-1470.2011.01586.x. Epub 2012 Feb 3.

Abstract

Blastic plasmacytoid dendritic cell neoplasm is an uncommon malignancy with a high incidence of cutaneous involvement, risk of leukemic dissemination, and poor prognosis. We report a 15-year-old boy with blastic plasmacytoid dendritic cell neoplasm who was treated with acute myeloid leukemia-based polychemotherapy and subsequent allogenic stem cell transplantation.

摘要

母细胞性浆细胞样树突状细胞肿瘤是一种罕见的恶性肿瘤,皮肤受累发生率高,有白血病播散风险,预后较差。我们报告一名15岁患有母细胞性浆细胞样树突状细胞肿瘤的男孩,他接受了基于急性髓系白血病的多药化疗及随后的异基因干细胞移植治疗。

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