Doğan A, Aksoy H
Osmaniye State Hospital, Cardiology Clinic, Osmaniye, Turkey.
Herz. 2012 Sep;37(6):699-701. doi: 10.1007/s00059-012-3582-4.
Noncompaction of the ventricular myocardium (NVM) is a rare cardiac anomaly which can lead to the development of cardiomyopathy. NVM can be isolated or associated with congenital heart anomalies such as ventricular septal defect, atrial septal defect, pulmonic stenosis, bicuspid aortic valve, and Ebstein anomaly. NVM usually presents with heart failure symptoms, ventricular tachyarrhythmias, and thromboembolic events. We report two cases of NVM, one associated with a ventricular septal defect and other associated with bicuspid aortic valve.
心室心肌致密化不全(NVM)是一种罕见的心脏异常,可导致心肌病的发生。NVM可以是孤立性的,也可与先天性心脏异常相关,如室间隔缺损、房间隔缺损、肺动脉狭窄、二叶主动脉瓣和埃布斯坦畸形。NVM通常表现为心力衰竭症状、室性快速心律失常和血栓栓塞事件。我们报告两例NVM病例,一例与室间隔缺损相关,另一例与二叶主动脉瓣相关。