Chung Hoyoung, Lilien Lawrence D
Pediatric Residency Program, Phoenix Children's Hospital, Phoenix, AZ 85016, USA.
Pediatr Cardiol. 2012 Apr;33(4):669-71. doi: 10.1007/s00246-012-0195-x. Epub 2012 Feb 4.
Total anomalous pulmonary venous connection is a cyanotic congenital heart defect that presents with a multitude of clinical presentations. We report a case of obstructive total anomalous pulmonary venous connection (TAPVC) which presented in a way that has not previously been described. An infant with mixed type obstructive TAPVC was found to have pulmonary interstitial emphysema and portal venous gas on a scout radiograph obtained prior to computed tomography scan. The presence of portal venous gas indicated a connection between the pulmonary venous system and the portal venous system infradiaphragmatically.
完全性肺静脉异位连接是一种伴有多种临床表现的青紫型先天性心脏缺陷。我们报告一例梗阻性完全性肺静脉异位连接（TAPVC）病例，其呈现方式此前未被描述过。一名患有混合型梗阻性TAPVC的婴儿在计算机断层扫描前获得的初步X线平片上被发现有肺间质肺气肿和门静脉积气。门静脉积气的存在表明肺静脉系统与膈下门静脉系统之间存在连接。
