Pesut Dragica, Stević Ruza, Milosavljević Jelica, Popević Spasoje, Cvok Tijana
Univerzitet u Beogradu, Medicinski fakultet, Beograd, Srbija.
Vojnosanit Pregl. 2011 Dec;68(12):1068-70. doi: 10.2298/vsp1112068p.
Mounier-Kuhn syndrome or tracheobronchomegaly is a rare disorder characterized by marked dilatation of the trachea and main bronchi, bronchiectasis, and recurrent respiratory tract infections. Its clinical presentation may vary and mimick a variety of disorders.
A 43-year-old female patient, non smoker, complained of intermittent mild dyspnea. Lung function tests and cardiologic findings were within normal limits. The diagnosis was established by computed tomography, which was undertaken due to recurrent lower respiratory tract infections suggestive of bronchiectasis. The transversal tracheal diameter was 2.8 cm that was the criteria for making the diagnosis. In this sporadic case, no association with other disease or condition known to cause secondary tracheobronchomegaly was established.
Although rare in clinical practice, Mounier-Kuhn syndrome is an impor tant differential diagnosis in cardio-pulmonary medicine due to a variety of its clinical manifestations. Nowadays, it is easy to diagnose it owing to advanced imaging techniques.
穆尼尔-库恩综合征或气管支气管巨大症是一种罕见的疾病，其特征为气管和主支气管显著扩张、支气管扩张以及反复的呼吸道感染。其临床表现可能各异，并可类似多种疾病。
一名43岁的女性患者，不吸烟，主诉间歇性轻度呼吸困难。肺功能测试和心脏检查结果均在正常范围内。因反复下呼吸道感染提示支气管扩张而进行的计算机断层扫描确诊了该病。气管横径为2.8厘米，这是做出诊断的标准。在这个散发病例中，未发现与其他已知可导致继发性气管支气管巨大症的疾病或状况有关联。
尽管在临床实践中罕见，但由于穆尼尔-库恩综合征有多种临床表现，它在心肺医学中是一个重要的鉴别诊断。如今，由于先进的成像技术，很容易对其进行诊断。
