Mercurella A, Galloni E, Danti S, Valli F, Colombo B, Belloli G
Divisione di Chirurgia Pediatrica, Ospedale Regionale, Vicenza, Italia.
Pediatr Med Chir. 1990 Mar-Apr;12(2):195-9.
The authors describe a rare case of primary intestinal lymphangiectasis resolved with surgical treatment. Usually the natural course of the disease is relatively mild and medical nutritional treatment can be sufficient. In this case the lymphatic intestinal anomaly was generalized to the entire small intestine but a distal ileal segment was particularly involved. The surgical resection of this intestinal tract resolved the symptomatology.
作者描述了一例通过手术治疗得以解决的原发性肠淋巴管扩张症罕见病例。通常，该病的自然病程相对较轻，医学营养治疗可能就足够了。在该病例中，肠道淋巴管异常累及整个小肠，但回肠远端部分受累尤为严重。对该肠道进行手术切除后症状得到缓解。
