Department of Medicine, Mercy Medical Associates, Batavia, OH 45103, USA.
Clin Chest Med. 2012 Mar;33(1):111-21. doi: 10.1016/j.ccm.2011.11.003.
Traditionally, a subset of patients diagnosed as having idiopathic pulmonary fibrosis had positive results on cellular biopsies (prominent lymphoplasmacytic inflammation), bronchoalveolar lavage lymphocytosis, a clinical response to steroids, and a better long-term prognosis. On review of the lung histopathology, the lesion was characterized by varying degrees of inflammation and fibrosis. This entity is now recognized as a distinct entity among idiopathic interstitial pneumonias.
传统上,一小部分被诊断为特发性肺纤维化的患者的细胞活检结果呈阳性(明显的淋巴浆细胞炎症)、支气管肺泡灌洗液淋巴细胞增多、对类固醇有临床反应和长期预后较好。回顾肺部组织病理学,病变的特征是不同程度的炎症和纤维化。该实体现在被认为是特发性间质性肺炎中的一个独特实体。