Segers J M
O.L. Vrouwkliniek, Oudenaarde.
Acta Otorhinolaryngol Belg. 1990;44(1):43-5.
A case of laryngeal stridor in an adult patient is presented and the diagnose of syndrome of Shy-Drager is proposed. This syndrome is the result of a degeneration of the central nervous system. Some autonomic functions are involved in this process. The leading symptoms are an orthostatic hypotension, parkinson-like symptoms and laryngeal stridor. The last symptom results from a neurogenic paralysis of both posterior crico-arytenoideus muscles. A depletion of neurotransmitters in the central nervous system would be the cause of the syndrome. The treatment is symptomatic. Concerning the laryngeal stridor, tracheotomy, eventually followed by a crico-arytenoidopexy, is the only treatment which can be proposed.
本文报告了一例成年患者的喉喘鸣病例,并提出了夏伊-德雷格综合征的诊断。该综合征是中枢神经系统变性的结果。这一过程涉及一些自主神经功能。主要症状为体位性低血压、帕金森样症状和喉喘鸣。最后一个症状是双侧环杓后肌神经源性麻痹所致。中枢神经系统中神经递质的耗竭可能是该综合征的病因。治疗以对症治疗为主。对于喉喘鸣,气管切开术,最终可能需要进行环杓关节固定术,是唯一可推荐的治疗方法。