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伴有蛋白异常血症的血管免疫母细胞性淋巴结病中的周围神经病变

Peripheral neuropathy in angioimmunoblastic lymphadenopathy with dysproteinaemia.

作者信息

Tredici G, Minazzi M, Lampugnani E

出版信息

J Neurol Neurosurg Psychiatry. 1979 Jun;42(6):519-23. doi: 10.1136/jnnp.42.6.519.

DOI:10.1136/jnnp.42.6.519
PMID:224148
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC490255/
Abstract

A case of angioimmunoblastic lymphadenopathy with dysproteinaemia complicated by a subacute peripheral neuropathy is described. Clinically the neuropathy was mainly motor, but pain and paraesthesiae in the legs were also present. Sural nerve biopsy indicated decreased numbers of myelinated fibres, mainly the largest, without actual signs of degeneration or regeneration. However, the occurrence of denervation bands indicated that degeneration had led to loss of myelinated fibres.

摘要

本文描述了一例血管免疫母细胞性淋巴结病伴蛋白异常血症并发亚急性周围神经病的病例。临床上,该神经病主要表现为运动障碍,但腿部也存在疼痛和感觉异常。腓肠神经活检显示有髓纤维数量减少,主要是最粗大的纤维,无实际的变性或再生迹象。然而,失神经带的出现表明变性已导致有髓纤维丧失。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1ca5/490255/11eb7ad8b18b/jnnpsyc00086-0038-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1ca5/490255/bf9b78cb8fd2/jnnpsyc00086-0037-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1ca5/490255/11eb7ad8b18b/jnnpsyc00086-0038-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1ca5/490255/bf9b78cb8fd2/jnnpsyc00086-0037-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1ca5/490255/11eb7ad8b18b/jnnpsyc00086-0038-a.jpg

相似文献

1
Peripheral neuropathy in angioimmunoblastic lymphadenopathy with dysproteinaemia.伴有蛋白异常血症的血管免疫母细胞性淋巴结病中的周围神经病变
J Neurol Neurosurg Psychiatry. 1979 Jun;42(6):519-23. doi: 10.1136/jnnp.42.6.519.
2
[Neuropathy in angioimmunoblastic lymphadenopathy (author's transl)].
Rev Neurol (Paris). 1981;137(8-9):503-15.
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[Angioimmunoblastic lymphadenopathy. Treatment of 2 cases].[血管免疫母细胞性淋巴结病。2例病例的治疗]
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[Angio-immunoblastic lymphadenopathy with dysproteinaemia (author's transl)].血管免疫母细胞性淋巴结病伴蛋白异常血症(作者译)
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本文引用的文献

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The neuropathy of multiple myeloma. An electrophysiological and histological study.
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Angio-immunoblastic lymphadenopathy with dysproteinaemia.血管免疫母细胞性淋巴结病伴蛋白异常血症
Lancet. 1974 Jun 1;1(7866):1070-3. doi: 10.1016/s0140-6736(74)90553-4.
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The morphological basis for alterations in nerve conduction in peripheral neuropathy.周围神经病变中神经传导改变的形态学基础。
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8
Letter: Chromosomes in AILD.信件:血管免疫母细胞性淋巴瘤中的染色体
N Engl J Med. 1975 May 1;292(18):975. doi: 10.1056/NEJM197505012921815.
9
Immunoblastic lymphadenopathy. A hyperimmune entity resembling Hodgkin's disease.免疫母细胞性淋巴结病。一种类似霍奇金病的高度免疫性疾病。
N Engl J Med. 1975 Jan 2;292(1):1-8. doi: 10.1056/NEJM197501022920101.
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Nerve biopsy and conduction studies in diabetic neuropathy.糖尿病性神经病变的神经活检与传导研究
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