Mordant P, Le Pimpec-Barthes F, Riquet M
Service de chirurgie thoracique, université Paris-5, hôpital européen Georges-Pompidou, Assistance publique-Hôpitaux de Paris, 20 rue Leblanc, Paris, France.
Rev Pneumol Clin. 2012 Apr;68(2):152-60. doi: 10.1016/j.pneumo.2012.01.013. Epub 2012 Mar 16.
Primary thoracic lymphatic diseases are both infrequent and probably under diagnosed. Current classification distinguishes lymphangioma (solitary tumor), lymphangiectasies (dilatation), lymphangiomatosis (proliferation) and lymphatic dysplasia syndrome (dysplasia). Classifications' efforts and radiologic progress may lead to an improvement in the management of these patients.