Genève J, Dubuc N, Mathieu D, Zafrani E S, Dhumeaux D, Métreau J M
Service d'Hépatologie et de Gastroentérologie, Hôpital Henri Mondor, Créteil, France.
J Hepatol. 1990 Sep;11(2):196-9. doi: 10.1016/0168-8278(90)90113-6.
A case of primary sclerosing cholangitis associated with cystic dilatations of intrahepatic bile ducts simulating Caroli's disease is described. The diagnosis of primary sclerosing cholangitis was based upon cholangiogram features, liver histologic examination and the association with chronic ulcerative colitis. It may be suggested that the cystic dilatation of intrahepatic bile duct represents an extreme form of the usual mild dilatations (cholangiectases) described in primary sclerosing cholangitis. We suggest that cystic dilatation of intrahepatic bile ducts could be included among the radiologic features of this disease.
本文描述了一例原发性硬化性胆管炎合并肝内胆管囊性扩张，类似卡罗利病（Caroli病）的病例。原发性硬化性胆管炎的诊断基于胆管造影特征、肝脏组织学检查以及与慢性溃疡性结肠炎的关联。可以认为，肝内胆管的囊性扩张代表了原发性硬化性胆管炎中常见的轻度扩张（胆管扩张症）的一种极端形式。我们建议肝内胆管囊性扩张可纳入该疾病的放射学特征之中。
