Institute of Reconstructive Plastic Surgery, New York University Langone Medical Center, New York, 10016-6497, USA.
Am J Crit Care. 2012 May;21(3):212-5. doi: 10.4037/ajcc2012904.
Aplasia cutis congenita, a rare congenital disorder involving defects of some or all of the layers of the cranium, is associated with potential life-threatening complications. Although treatment involves both nonsurgical and surgical techniques, the importance of perioperative management cannot be overstressed. A multidisciplinary team, including personnel from nursing, neonatology, pediatrics, radiology, neurosurgery, and plastic surgery services, diagnosed aplasia cutis congenita and planned local wound care, surgical correction, and prevention of potentially life-threatening complications in a 1-day-old boy with a 6×5-cm full-thickness scalp defect.
先天性皮肤发育不全是一种罕见的先天性疾病，涉及颅骨的部分或全部层的缺陷，与潜在的危及生命的并发症有关。尽管治疗涉及非手术和手术技术，但围手术期管理的重要性怎么强调都不为过。一个多学科团队，包括来自护理、新生儿科、儿科、放射科、神经外科和整形外科的人员，诊断了一名 1 天大的男孩患有 6×5 厘米全层头皮缺损的先天性皮肤发育不全，并计划进行局部伤口护理、手术矫正和预防潜在危及生命的并发症。
