Division of Pediatric Neurology and Developmental Pediatrics, Department of Pediatrics, Postgraduate Institute of Medical Education and Research PGIMER, Chandigarh 160012, India.
Indian J Pediatr. 2013 Jun;80(6):509-12. doi: 10.1007/s12098-012-0771-3. Epub 2012 May 10.
Primary intracranial ependymal cysts are congenital, benign, ependyma-lined cysts rarely seen in the pediatric age group. The authors report such a case of intracranial fronto-parietal ependymal cyst in a 3 y-old girl. Computed tomography showed a large cystic lesion which was not in communication with the ventricular system and was associated with ipsilateral posterior cerebral artery infarct and raised intracranial pressure causing midline shift. A differential diagnosis of the commoner arachnoid, hydatid or porencephalic cyst was considered. Surgical removal to decompress the brain was done; histopathology revealed an ependymal cyst. Identification of this rare pathology in the pediatric age group is emphasized with a review of the literature.
原发性颅内室管膜囊肿是一种罕见的先天性、良性、室管膜衬里的囊肿，主要见于儿童。作者报告了一例 3 岁女孩的颅内额顶叶室管膜囊肿。计算机断层扫描显示一个大的囊性病变，与脑室系统无交通，与同侧大脑后动脉梗死和颅内压升高导致中线移位有关。考虑了更常见的蛛网膜囊肿、包虫囊肿或脑穿通畸形囊肿的鉴别诊断。为了减轻脑压进行了手术切除；组织病理学显示为室管膜囊肿。本文强调了在儿童期识别这种罕见病理的重要性，并对文献进行了回顾。
