Low-grade central osteosarcoma of the orbit.

Low-grade central osteosarcoma is a rare type of osteosarcoma, representing fewer than 2% of all osteosarcomas. Approximately 80% of these tumors are located in the long bones, and they are particularly common in the distal and proximal tibia. However, they are rare in the craniofacial bones, and this tumor type has never been reported to occur in the orbit. In this report, a case of low-grade central osteosarcoma arising from the orbit is presented. The differential diagnoses of this tumor and the surgical results of radical resection and reconstruction are also presented.