心脏内恶性纤维组织细胞瘤。病例报告。
Intracardiac malignant fibrous histiocytoma. A case report.
作者信息
Urías-Báez Rafael, de la Cerda-Belmont Gustavo, Cuevas-Domínguez Agustín, Careaga-Reyna Guillermo
机构信息
Departamento de Cirugía Cardiotorácica. UMAE, Hospital General Dr. Gaudencio González Garza, Centro Médico Nacional La Raza, IMSS, México, D.F., Mexico.
出版信息
Cir Cir. 2012 Mar-Apr;80(2):182-5.
BACKGROUND
Primary cardiac tumors are rare forms of cardiac disease. The reported incidence varies between 0.002 and 0.3%; 25% of these tumors are malignant, usually a variant of sarcoma. Malignant fibrous histiocytoma constitutes <3% of primary cardiac tumors.
CLINICAL CASE
We review the case of a 53-year-old female who presented with congestive heart failure and pleural effusion. Transthoracic echocardiography and chest computed tomography revealed cardiac tumor involving the left atrium. Tumor was excised surgically and histologically proven to be a malignant fibrous histiocytoma, primarily confined to the heart. During the immediate postoperative evolution, the patient presented left pleural effusion for 2 weeks. The patient was referred to Oncology Service for complementary treatment.
CONCLUSION
Malignant fibrous histiocytoma is a rare tumor and, in this case, prognosis is reserved.
背景
原发性心脏肿瘤是心脏病的罕见形式。报道的发病率在0.002%至0.3%之间；其中25%的肿瘤是恶性的，通常是肉瘤的一种变体。恶性纤维组织细胞瘤占原发性心脏肿瘤的比例不到3%。
临床病例
我们回顾了一名53岁女性的病例，该患者出现充血性心力衰竭和胸腔积液。经胸超声心动图和胸部计算机断层扫描显示心脏肿瘤累及左心房。肿瘤通过手术切除，组织学证实为恶性纤维组织细胞瘤，主要局限于心脏。术后即刻恢复过程中，患者出现左侧胸腔积液持续2周。患者被转至肿瘤科进行辅助治疗。
结论
恶性纤维组织细胞瘤是一种罕见肿瘤，在本病例中，预后不容乐观。
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