因子 X 缺乏：AL 淀粉样变性的一种不常见表现。
Factor X deficiency: an uncommon presentation of AL amyloidosis.
机构信息
Emory University Hospital, 1364 Clifton Road NE, Atlanta, GA 30322, USA.
出版信息
Ups J Med Sci. 2012 Nov;117(4):457-9. doi: 10.3109/03009734.2012.690457. Epub 2012 Jun 1.
Abstract
Factor X deficiency is the most common coagulation factor deficiency amongst patients with AL amyloidosis. It presumably occurs due to adsorption of factor X to amyloid fibrils. The deficiency of this factor, in conjunction with other hemostatic defects, can cause bleeding complications. A case of acquired factor X deficiency due to AL amyloidosis is reported, where abnormal coagulation parameters were the only presenting feature.
摘要
因子 X 缺乏症是 AL 淀粉样变性患者中最常见的凝血因子缺乏症。它可能是由于因子 X 吸附到淀粉样纤维上而发生的。这种因子的缺乏，加上其他止血缺陷，可能导致出血并发症。报告了一例由 AL 淀粉样变性引起的获得性因子 X 缺乏症，其中异常的凝血参数是唯一的表现特征。
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