Salunke Pravin, Futane Sameer S, Aggarwal Ashish
Department of Neurosurgery, Postgraduate Institute of Medical Education & Research, Chandigarh, India.
J Neurosurg Pediatr. 2012 Jun;9(6):627-9. doi: 10.3171/2012.2.PEDS11498.
Although uncommon, variations in split cord malformation (SCM) have been described. However, a combination of SCM Type II and dorsal lipomas has not been reported. The authors describe the case of a 6-year-old girl who presented with a 1-year history of spastic paraparesis associated with a lipomatous swelling on her lower back. Radiology revealed a Type II SCM with a dorsal lipoma at that level. Intraoperatively, the authors observed a dorsal lipoma for each hemicord; these were excised, and the septum causing the split was cut. Premature separation of the cutaneous and neural ectoderm is predetermined for each neural fold, and a split at this level would give rise to SCM with twin dorsal lipomas, one for each hemicord.
尽管脊髓纵裂畸形（SCM）的变异情况并不常见，但已有相关描述。然而，II型SCM与背部脂肪瘤并存的情况尚未见报道。作者报告了一例6岁女孩的病例，该女孩有1年痉挛性截瘫病史，同时下背部有脂肪瘤样肿胀。影像学检查显示该水平存在II型SCM并伴有背部脂肪瘤。术中，作者观察到每个半脊髓均有一个背部脂肪瘤；将这些脂肪瘤切除，并切断导致脊髓纵裂的中隔。每个神经褶的皮肤和神经外胚层过早分离是预先确定的，在此水平的纵裂会导致伴有双侧背部脂肪瘤的SCM，每个半脊髓各有一个。
