Neurol Sci. 2013 May;34(5):785-8. doi: 10.1007/s10072-012-1122-x. Epub 2012 Jun 4.
Non-parenchymal neuro-Behçet disease generally affects cerebral venous sinuses, whereas intracranial intracerebral arterial involvement has been rarely reported. But co-involvement of both intracranial intracerebral artery and venous vascular systems in a patient at the same time has not been mentioned before. To the best of our knowledge, this case involving a 25-year-old male with a 7-year history of Behçet disease is the first reported of this type of involvement. He developed occlusion of the basilar artery together with thrombosis of the left sigmoid sinus, distal internal jugular vein, and straight sinus. He was successfully treated with a combination of high-dose steroid and cyclophosphamide. Cranial magnetic resonance angiography demonstrated the resolution of these abnormalities.
非实质神经贝赫切特病一般影响脑静脉窦,而颅内脑动脉受累则很少见报道。但是,同时累及颅内脑动脉和静脉血管系统在同一患者中尚未提及。据我们所知,本例涉及一名 25 岁男性,患有贝赫切特病 7 年,是首例此类受累的报道。他发生基底动脉闭塞,同时伴有左侧乙状窦、远段颈内静脉和直窦血栓形成。他成功地接受了大剂量类固醇和环磷酰胺联合治疗。头颅磁共振血管造影显示这些异常得到了缓解。